【摘 要】
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Backgroud Ehlers-Danlos Syndrome (EDS) is a rare group of inheritable disorders resulting in abnormal collagen production,leading to skin fragility,joint hypermobility and easy bruising.In the rare va
【机 构】
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Department of Neurology,Huashan Huashan Hospital Affiliated to Fudan University
论文部分内容阅读
Backgroud Ehlers-Danlos Syndrome (EDS) is a rare group of inheritable disorders resulting in abnormal collagen production,leading to skin fragility,joint hypermobility and easy bruising.In the rare vascular type of EDS there is a defect in the synthesis of collagen type Ⅲ,important constituent of the blood vessel wall,which may cause arterial rupture,dissection and neurovascular complications.
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