多囊肾病为遗传性疾病,根据其遗传特征可分为婴儿型与成人型两大类。婴儿型是常染色体隐性遗传病,比较少见,患儿大多在出生后不久死亡。成人型是肾囊性病变中最常见的一种类型,以常染色体显性遗传在家族中传递。成人多囊肾(ADPKD)为慢性肾功能衰竭的第三位原因,占住院血透的移植病人的5～ Polycystic kidney disease is a genetic disease, according to their genetic characteristics can be divided into two categories of infant and adult type. Infantile type is autosomal recessive genetic disease, relatively rare, most of the children died after birth. Adult type is the most common type of renal cystic lesions, transmitted by an autosomal dominant inheritance in the family. Adult polycystic kidney disease (ADPKD) is the third cause of chronic renal failure, accounting for transplanted hemodialysis patients 5 ~