患者女,8岁。右侧腹股沟外侧一红色丘疹8年,渐增大,近半年增大明显。皮损组织病理示:肿瘤位于真皮及皮下,由大小不等的呈囊状扩张的薄壁管腔构成,囊性扩张的薄壁管腔内见鞋钉样内皮细胞,肿瘤细胞排列呈乳头状、肾小球样向腔内突出,核分裂相少见。结合临床、组织病理及免疫组织化学染色诊断为乳头状淋巴管内血管内皮细胞瘤。 Female patient, 8 years old. The right side of the groin outside a red papules 8 years, gradually increased, increased significantly in the past six months. Histopathology of the lesion showed that the tumor was located in the dermis and subcutaneous and consisted of cystic dilated thin-walled lumens ranging in size. In the cystic dilated thin-walled lumen, the cleft-like endothelial cells were seen, and the tumor cells arranged in a papillary , Glomerulus like to the cavity prominent, mitotic phase rare. Combined with clinical, histopathological and immunohistochemical staining for diagnosis of papillary intravascular lymphatic endothelial angioma.