肾血管平滑肌脂肪瘤(RAML)是肾的一种错构瘤,约占全部肾肿瘤的2·0%~6·4%,是最常见的肾脏良性肿瘤,可单发、多发或双侧发病,双侧发病者通常伴发结节性硬化症,属常染色体显性遗传。但恶性生物学行为的RAML国内外罕有报道,我科共收治2例,现报告如下。1临床资料2例均为成年男性患 Renal angiomyolipoma (RAML), a hamartoma of the kidney accounting for 2.0% to 6.4% of all renal tumors, is the most common benign renal neoplasm and can be single, multiple or bilateral , Bilateral disease are usually associated with tuberous sclerosis, is an autosomal dominant. However, malignant biological behavior of RAML rarely reported at home and abroad, our department received a total of 2 cases, are as follows. 1 clinical data 2 cases were adult male patients