原发性限制型心肌病多见于青少年,其特征为心室内膜和内层心肌、乳头肌进行性纤维化,导致心室的硬化和狭窄。本病的临床表现与心包病变尤其是缩窄性心包炎极为相似。临床少见,国内仅有个案报道,且生前作出诊断者更少。我院见到一例,报告如下: 患者男,16岁,学生,住院号32374,1980年10月23日入院。自同年6月始,发冷、发 Primary limiting cardiomyopathy is more common in adolescents and is characterized by progressive fibrosis of the ventricular and inner myocardium, papillary muscles leading to ventricular cirrhosis and stenosis. The clinical manifestations of this disease and pericardial lesions, especially constrictive pericarditis is very similar. Clinically rare, there are only cases reported in China, and make fewer diagnoses during their lifetime. One case was seen in our hospital. The report was as follows: Patient male, 16 years old, student, hospital number 32374, admitted to hospital on October 23, 1980. Since the same year in June, chills, hair