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目的 探讨Gorham Stout综合征的X线表现特点 ,以期提高对本病X线诊断的认识水平 ,有助于与其他溶骨性改变的疾患鉴别。材料与方法 3例经病理证实的Gorham Stout综合征 ,其中单发于肋骨 2例 ,肋骨、肱骨、肩胛骨多发 1例。回顾性研究其X线表现 ,结合国内外文献资料 ,分析其X线诊断及鉴别诊断要点。结果 3例均呈进行性大片骨质溶解破坏 ;长骨破坏区残端削尖变细 ,无骨膜反应及新骨形成 ,无软组织肿块 ,病理性骨折不愈合等X线征象 ,具有一定病变特征。结论 Gorham Stout综合征的X线表现具有特征性。结合病史特点 ,X线可提示本病的诊断 ,但须排除其他可引起溶骨性改变的疾病
Objective To investigate the X-ray features of Gorham Stout syndrome in order to improve the level of understanding of the X-ray diagnosis of the disease and to help with the identification of other diseases with osteolytic changes. Materials and Methods Three cases of pathologically confirmed Gorham Stout syndrome, including single rib in 2 cases, rib, humerus, scapular multiple in 1 case. Retrospective study of its X-ray findings, combined with domestic and foreign literature, X-ray diagnosis and differential diagnosis points. Results All the 3 cases showed progressive massive osteolysis and destruction. The remnant of the long bone destruction area was sharpened, no periosteal reaction and new bone formation, no soft tissue mass, nonunion of pathological fracture and other X-ray signs. Conclusion Gorham Stout syndrome has characteristic X-ray findings. Combined with the history of the disease, X-ray can prompt the diagnosis of the disease, but to exclude other diseases that can cause osteolytic changes