先天性角膜感觉缺失症是一种少见病。常在生后一年或二年出现角膜混浊或溃疡,用表面药物治疗无效,需作眼睑缝合术来阻止上皮的破裂。作者报告一例用 Cochet-Bonnet 氏感觉测定仪确诊和治疗中用亲水软镜治疗的双眼先天性角膜感觉缺失症。患者6岁男孩,双眼视力不佳和畏光数年,在两岁时肥皂水曾溅入右眼,药物治愈后遗留下小瘢痕和 Congenital corneal ataxia is a rare disease. Often one or two years after birth, corneal opacities or ulcers, with the surface of the drug treatment is invalid, the need for eyelid suture to prevent epithelial rupture. The authors report a case of congenital keratosis in both eyes treated with hydrophilic soft-lens in the diagnosis and treatment with the Cochet-Bonnet’s sensory analyzer. 6-year-old boy with poor binocular vision and photophobia for several years had soapy water splashed into the right eye at two years of age and left little scarring after the drug was cured