迟发性皮肤型卟啉病属肝性卟啉病,是欧美最常见的一种卟啉代谢病,以肝脏产生和贮藏过量的卟啉为特征.本文报导了1960～1976年间对40例病人经4月～7年观察的临床和实验室资料.40例中,男性17例,平均发病年龄44.2岁;女性23例,平均发病年龄46.5岁.在病因方面,饮酒是男性最重要的原因,占65%;而服用雌激素或同时并用酒精是女性的主要病因;占61%.仅2例有家族史.皮损好发于露出部位,包括水疱、大疱(85%), Delayed skin type porphyria is a hepatic porphyria which is one of the most common porphyria metabolic diseases in Europe and the United States and is characterized by liver production and storage of excess porphyrins.This paper reports the clinical data of 40 patients Clinical and laboratory data were observed from April to July 2007. Of the 40 cases, 17 were males, with an average age of 44.2 years and 23 females, with an average age of 46.5 years old. In terms of etiology, drinking was the most important cause of males, Accounting for 65%; while taking estrogen or at the same time with alcohol is the main cause of women, accounting for 61%, only 2 cases have a family history of skin lesions occur in the exposed parts, including blisters, bullous (85%),