系统性血管炎由于受累血管部位及大小不同，临床表现多样，而且由于分类较为混乱而无统一标准，故经常造成诊断上的困难。目前广泛采用的仍为１９９４年ＣｈａｐｅｌＨｉｌ分类标准〔１〕，它将有坏死性小血管（小动脉、毛细血管、小静脉）炎者，称之为显微镜下多血管炎（... Systematic vasculitis due to involvement of different vascular sites and sizes, clinical manifestations, and because the classification is more confusion without a uniform standard, it often causes diagnostic difficulties. Currently widely used still ChapelHil 1994 classification criteria 〔1〕, it will have necrotizing small blood vessels (arterioles, capillaries, small veins) inflammation, called microscopic polyangiitis (...