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目的：提高对Ｌａｒｓｅｎ综合征的诊断及治疗水平。方法：５例患儿，男２例，女３例，年龄２～８岁。主要临床表现：５例均有颜面扁平、眼距增宽、鼻梁塌陷，伴有多关节脱位，主要累及双髋、双膝、双肘和双髌骨。１例２岁双髋关节脱位行软组织松解，手法复位；２例４岁双髋关节脱位行切开复位，Ｓａｌｔｅｒ骨盆截骨和股骨旋转截骨；２例膝关节、３例髌骨脱位行外侧软组织松解，内侧关节囊紧缩，股内侧肌止点移向髌骨前外侧，外侧１／２髌韧带止点内移。结果：术后随访时间１～３年，关节复位，功能良好。结论：Ｌａｒｓｅｎ综合征有典型的临床特征，可早期诊断。对关节脱位给予正确治疗，可获得良好的复位和功能。
Objective: To improve the diagnosis and treatment of Larsen’s syndrome. Methods: Five cases of children, 2 males and 3 females, aged 2 to 8 years old. The main clinical manifestations: 5 cases were flat face, widened eyes, bridge collapse, with multiple joint dislocation, mainly involving double hip, knees, double elbows and double patella. One case of 2-year-old double hip joint dislocation had soft tissue release and manual reduction. Two cases of 4-year-old double hip joint dislocation underwent open reduction, Salter pelvic osteotomy and femoral osteotomy. Two knees and three lateral patellar dislocation Soft tissue release, medial joint capsule tightening, medial part of the medial patella only point to the lateral lateral patellar lateral patellar shift, Results: Follow-up time 1-3 years, joint reset, good function. Conclusion: Larsen’s syndrome has typical clinical features and can be diagnosed early. Correct dislocation of the joint treatment, access to a good reset and function.