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本文报告一例合并有颜面部血管瘤的Ｃｏｇａｎ－Ｒｅｅｓｅ综合征，讨论了该病的临床生理学特点及发病机制。角膜内皮细胞异常增生形成的细胞性膜为原发病变，虹膜改变及虹膜前粘连属继发病变，支持角膜内皮细胞异常是由于神经嵴细胞组织发生异常增殖的学说。治疗主要针对眼压升高及角膜水肿，降眼压是基本措施，滤过性手术可早期施行。
This article reports a case of Cogan-Reese syndrome with facial hemangiomas and discusses the clinical features and pathogenesis of the disease. Corneal endothelial cell dysplasia formed by the formation of the primary membranous membrane of the lesion, iris changes and pre-iris adhesions is a secondary lesion, support for corneal endothelial cell abnormalities is due to neural crest cells abnormal proliferation theory. Treatment is mainly aimed at intraocular pressure and corneal edema, IOP reduction is the basic measure, filtration surgery can be implemented early.