共济失调毛细血管扩张症又称毛细血管扩张性共济失调.多系常染色体隐性遗传,国内报告较少,现报告2例如下.例1.男,10岁.以走路不稳8年,加重1年入院.痴呆貌,反应迟纯,问答不流利,头部有片状脱发,皮肤有色素脱失斑及色素沉着,双眼球结膜毛细血管扩张明显,双眼粗大水平震颤,心肺正常,肝脾 Ataxia telangiectasia, also known as telangiectasia ataxia. Multi-line autosomal recessive inheritance, fewer domestic reports, the report 2 cases are as follows .Example 1. Male, 10 years old. To walk for 8 years , Aggravating 1 year admission.Dementia appearance, reaction is not pure, question and answer is not fluent, the head has flake hair loss, pigmentation and pigmentation of skin pigmentation, conjunctival capillaries dilated obviously, eyes coarse level tremor, cardiorespiratory normal, Liver and spleen