腺泡样软组织肉瘤是一类罕见的软组织肉瘤,具有一定的组织学特异性,肿瘤细胞的分化水平不一,临床表现多样。该病主要发生于青少年和年轻成人,女性多见。头颈部发病少见,且以舌和眼眶为主,而发生于颊部者极为罕见。本文报告1例颊部腺泡样软组织肉瘤,并结合文献对其临床表现、诊断、组织学特点、治疗及预后进行讨论。 Acinar soft tissue sarcoma is a rare type of soft tissue sarcoma, has a certain histological specificity, the level of differentiation of tumor cells, clinical manifestations and diverse. The disease occurs mainly in adolescents and young adults, more common in women. Head and neck rare disease, and to the tongue and orbital, and occurred in the cheeks are extremely rare. This article reports 1 case of buccal acinar soft tissue sarcoma, and combined with the literature on its clinical manifestations, diagnosis, histological features, treatment and prognosis are discussed.