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1957年 Jervell 等首次描述了先天性耳聋、Q—T 间期延长、由于室性纤颤发生晕厥而突然死亡的综合征,1966年他和Thingstad 等把同样的病例命名为心脏—听觉或耳聋—心脏(Surdo-Cardiac)综合征。相继由 Romano 和 Ward 发现不伴耳聋的类似病例,并把无先天性耳聋的 Q-T 间期延长命名为 Romano-Ward 综合征。后来Moss 等和 Jams 报道了特发性 Q-T 间期延长综合征(以下简称 Q-T 综合征)突然死亡。Roy 等观察了三家遗传性 Q-T 综合征的12名者患,有三例突然死亡,其中一例死于睡眠中。最近 Wig 等报道一例 Q—T 综
In 1957 Jervell et al. First described the syndrome of congenital deafness, Q-T prolongation and sudden death due to syncope of ventricular fibrillation. In 1966 he and Thingstad et al. Named the same patient as heart-hearing or deafness- Surv-Cardiac syndrome. A similar case without deafness was found by Romano and Ward one after another, and the Q-T prolongation without congenital deafness was named Romano-Ward syndrome. Later Moss et al. And Jams reported a sudden death of idiopathic Q-T prolongation syndrome (hereinafter referred to as Q-T syndrome). Roy et al. Observed 12 patients with three hereditary Q-T syndromes. Three died suddenly and one died of sleep. Wig recently reported a case of Q-T comprehensive