一、全丙种球蛋白低下血症(Panhypogamma globulinemia简称全低丙球血症):低丙种球蛋白血症包括全丙种球蛋白低下血症和选择性某类(或亚类)免疫球蛋白缺陷症。三类主要免疫球蛋白(IgG、IgA、IgM)都低下的原发性全低丙球血症临床上分为三型:(1)常见的型是X-伴性遗传,即Bruton氏病(1952年首例报告)。缺乏B细胞,4～8月龄起病,此时通过胎盘由母体提供的IgG已所余无几, First, all hypogammaglobulinemia (Panhypogamma globulinemia referred to as all low-grade plasmaprolactine): low gammaglobulinemia, including all gamma globulin hypoproteinemia and selective class (or subclass) immunoglobulin deficiency . Three types of major immunoglobulin (IgG, IgA, IgM) are low-grade primary total plasma propofol is clinically divided into three types: (1) common type is X-associated inheritance, that is, Bruton’s disease 1952 first report). Lack of B cells, 4 to 8 months of age, this time through the placenta provided by the mother has been depleted of IgG,