视网膜色素变性是以视网膜的进行性变性伴有夜盲、视野缺损为特征的一种遗传性疾病。1857年由Donder命名为“色素性视网膜炎”(retinitis pigmentosa)。实际上,它是视网膜色素上皮和视网膜光感受器的变性。因此,“炎”的命名是不恰当的。一、发病率有关视网膜色素变性(简称RP)的发病率,目前缺乏精确的统计。英国为1- Retinitis pigmentosa is a progressive degeneration of the retina with night blindness, visual field defect is characterized by a genetic disease. In 1857 Donder named “retinitis pigmentosa.” In fact, it is a degeneration of the retinal pigment epithelium and retinal photoreceptors. Therefore, the name of “inflammation” is not appropriate. First, the incidence of retinitis pigmentosa (RP) incidence, the current lack of accurate statistics. United Kingdom for 1-