目的总结肺错构瘤的诊断和治疗经验。方法1例腔内型错构瘤在纤维支气管镜下行肿物摘除术,余42例行胸腔镜或胸腔镜辅助小切口手术,其中肺楔形切除40例,肺叶切除1例,双侧病灶活检1例。结果43例病理均为错构瘤,其中1例为多发性肺错构瘤,1例肺癌合并肺错构瘤。术后病理诊断与术前诊断符合率11.6%(5/43)。37例随访4个月~11年,平均41.2月,无复发与恶变。结论肺错构瘤术前难以确诊,腔镜手术可以提供明确的诊断并能彻底切除病灶,创伤小,恢复快。 Objective To summarize the diagnosis and treatment of pulmonary hamartoma. Methods One case of intracavitary hamartoma underwent resection of the tumor by fiberoptic bronchoscopy. Thirty-two patients underwent thoracoscopic or thoracoscopic assisted small incision surgery, including 40 cases of wedge resection, 1 case of lobectomy, 1 case of bilateral lesion biopsy example. Results 43 cases were pathological hamartoma, including 1 case of multiple pulmonary hamartoma, 1 case of lung cancer with pulmonary hamartoma. Postoperative pathological diagnosis and preoperative diagnosis in line with the rate of 11.6% (5/43). 37 cases were followed up for 4 months to 11 years, an average of 41.2 months, no recurrence and malignant transformation. Conclusion Pulmonary hamartoma is difficult to diagnose before operation. Endoscopic surgery can provide a definite diagnosis and complete removal of the lesion with less trauma and rapid recovery.