原发于不见节细胞外周神经的神经母细胞瘤颇罕见,现报告一例。患者,男,18岁。左侧臀部于5年前有一拳大包块,以后逐渐增大,影响左下肢活动,局部检查表面皮肤组织无破溃,行局部肿物切除。病理巨体观:一侧附有少量皮肤的肿物一个,重3250g,大小为23×10.5×19cm,结节状,包膜不完整,切面鱼肉状,内有腐烂、出血,临床诊断:横纹肌肉瘤。组织学检查:血管丰富,瘤细胞圆 Neuroblastomas that originate in non-segmental peripheral neurons are rare and are now reported. Patient, male, 18 years old. The hip on the left had a massive mass five years ago. Afterwards, it gradually increased, affecting the activities of the left lower extremities, and partially examining the surface skin tissue without ulceration. Local tumor removal was performed. Pathological macroscopic view: a tumor with a small amount of skin on one side, weighing 3250g, the size of 23 × 10.5 × 19cm, nodular, incomplete capsule, cut surface fish-like, with rot, hemorrhage, clinical diagnosis: rhabdomyosarcoma . Histological examination: rich blood vessels, tumor cells round