目的　探讨脉络膜前动脉远端动脉瘤 (DAChAA)的诊断与治疗。方法　报告 1例病人的临床资料 ,并复习文献 2 1例。结果　患者头颅CT检查示脑室内出血 (IVH) ,经数字减影脑血管造影 (DSA)确诊 ,手术及病理证实为脑室内DAChAA ,经手术治愈。文献 2 1例DAChAA中 1 3例伴发于颅内烟雾病 ,2 0例发生颅内出血 ,多为IVH(9例 ) ,次为脑内血肿 (ICH) (6例 ) ,均靠脑DSA确诊 ,手术切除动脉瘤 (AN) 7例中 ,3例疗效良好。结论　DAChAA罕见 ,治疗困难 ,但只要处理得当 ,有望治愈 Objective To investigate the diagnosis and treatment of anterior anterior communicating artery aneurysms (DAChAA). Methods One patient’s clinical data was reported and 21 patients were reviewed. Results The head CT examination showed intraventricular hemorrhage (IVH), confirmed by digital subtraction angiography (DSA), and confirmed by surgery and pathology as intracerebral DAChAA after operation. In the literature, 13 cases of DAChAA complicated with intracranial moyamoya disease and 20 cases of intracranial hemorrhage were mostly IVH (9 cases) and intracerebral hematoma (ICH) (6 cases), all of which were diagnosed by brain DSA Among the 7 cases with surgical resection of aneurysm (AN), 3 cases were effective. Conclusions DAChAA is rare and difficult to treat, but as long as it is properly treated, it is expected to be cured