自从1957年Sament等报告本综合征以来,国内外文献报告的病例日益增多。到1973年止,已超过200例。许多作者还指出实际病例数比文献中已报告的要多。由于本综合征与糖尿病酮症性昏迷在处理上有很多不同之处,而过去对它认识不足,故现将本综合征的临床特征、实验室检查、发病机理、诊断和治疗综述如下。 Since Salary et al. Reported this syndrome in 1957, the number of cases reported in domestic and foreign literature has been increasing. By 1973, there were more than 200 cases. Many authors also point out that the actual number of cases is more than what has been reported in the literature. Because of this syndrome and diabetic ketoacidosis in the handling of many differences, but in the past its lack of knowledge, so now the clinical features of this syndrome, laboratory tests, pathogenesis, diagnosis and treatment are summarized below.