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目的了解脑膜血管瘤病(meningioangiomatosis,MA)的临床及病理特点。方法对1例MA患者进行临床分析及鉴别诊断,依靠脑组织活检,病理确诊为MA,复习文献并总结其临床及病理特点。结果 MA发病年龄多在10~30岁。患者常伴有癫痫发作,常见全面强直阵挛发作。影像学检查头颅CT示病灶内部斑点状或絮状钙化,头颅MRI示等T1信号,T2和FLAIR相上病灶表现为混杂信号,病变周围几乎没有水肿和占位效应,强化扫描MA病变通常只有轻微的或没有强化。确诊依赖于活检。结论根据患者的发病年龄、癫痫发作类型以及CT和MR的影像学检查可以从临床角度考虑脑膜血管瘤病的诊断。
Objective To investigate the clinical and pathological features of meningioangiomatosis (MA). Methods The clinical data and differential diagnosis of one patient with MA were analyzed. The brain tissues were biopsied and the pathology was diagnosed as MA. Review the literature and summarize its clinical and pathological features. Results MA age of onset more than 10 to 30 years old. Patients often accompanied by seizures, common full tonic clonic seizures. Radiographic examination of cranial CT showed focal spots or flocculent calcification within the lesion, cranial MRI showed T1 signal, T2 and FLAIR phase lesions showed mixed signals, lesions almost no edema and space-occupying effect, enhanced scan MA lesions are usually only mild Or not strengthened. Diagnosis depends on biopsy. Conclusions The diagnosis of meningeal hemangiomatosis can be considered clinically based on the patient’s age of onset, type of seizure, and CT and MR imaging.