食道内脏型神经纤维瘤病致先天性食道狭窄１例报告平小佳（第一附属医院病理科）患者，男，４岁，汉族。出生至今只能进流汁，２年前曾呕吐血性分泌物，出现黑便。胸片示：食道下段环形狭窄，约５０ｍｍ长，狭窄上段食道明显扩张，诊断为贲门失弛缓症，先天性食道下段狭窄... One case of congenital esophageal stenosis caused by esophageal visceral neurofibromatosis was reported by Ping Xiaojia (Department of Pathology, First Affiliated Hospital), male, 4 years old, Han nationality. He was only able to drink juice at the time of birth. He had vomited bloody secretions two years ago and developed black stools. Chest radiograph: the lower esophagus ring is narrow, about 50mm long, the upper esophagus of the stenosis is significantly dilated, diagnosed as achalasia, congenital esophageal stenosis...