目的 探讨眼部神经鞘瘤的临床诊断和病理特征及其治疗。方法 对56例眼部神经鞘瘤住院患者的临床、影像学特点、病理资料和手术情况进行分析。结果 56例均经病理证实为眼部神经鞘瘤,30-50岁多见,占55.4％,多发于肌锥内及眼眶上方,56例手术全切除,其中经前路开眶肿瘤摘除术38例,侧壁开眶肿瘤摘除术14例,眼球摘除术3例,睫状体肿瘤摘除1例,术后随访6个月至12年,2例复发。结论 眼部神经鞘瘤诊断要结合临床及CT、彩超等影像学检查,手术全切除为主要治疗方法。 Objective To investigate the clinical diagnosis and pathological features of optic nerve schwannoma and its treatment. Methods The clinical, imaging characteristics, pathological data and operation of 56 patients with schwannoma of the eye were analyzed. Results 56 cases were pathologically confirmed as schwannoma of the eye, 30-50 years old more common, accounting for 55.4%, mainly in the muscle and the orbit above the eye, 56 cases of total resection, of which anterior orbital tumor resection 38 Cases, 14 cases of lateral orbital tumor resection, enucleation in 3 cases, ciliary body tumor removal in 1 case, followed up for 6 months to 12 years, 2 cases of recurrence. Conclusion The diagnosis of ocular schwannoma should be combined with clinical and CT, color Doppler ultrasound imaging, total excision as the main treatment.