作者回顾性复习5例患镰形细胞性肾髓质癌的临床、病理和放射学资料以及放射学所见与大体病理所见的关系。男2例,女3例,年龄10～28岁。根据最初诊断时获得放射学资料和手术所见确定肿瘤分期。用血红蛋白电泳确定有镰形细胞特性或肾脏切片组织学中见到有镰形红细胞。最初的临床表现包括;季肋部疼痛(3例)、体重减轻(1例)、腹部包块(1例)、不明原因发烧(1例)、血尿(2例)、肝脏酶学增高和白细胞数增多(1例)。根据在肾髓质中形成明显肿块、在皮质和接近肾门处常常伴有小的星状结节作 The authors retrospectively reviewed the clinical, pathological and radiographic data of 5 patients with sickle cell renal medullary carcinoma and the relationship between radiographic evidence and gross pathology. 2 males and 3 females, aged 10 to 28 years old. Determine the tumor staging based on radiological data and surgical findings from the initial diagnosis. Sickle cell characteristics were identified by hemoglobin electrophoresis or sickle cell erythrocytes were seen in histology of kidney sections. The initial clinical manifestations include: quarter rib pain (3 cases), weight loss (1 case), abdominal mass (1 case), unexplained fever (1 case), hematuria (2 cases), liver enzymatic increase and white blood cells Number increased (1 case). According to the formation of significant medulla mass in the cortex and close to the renal portal often accompanied by a small stellate nodules