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上皮样肉瘤是软组织肉瘤中一种非常罕见的组织学类型,常表现为青少年肢体远端的皮下组织或真皮内肿物。其中有一型具有较高的侵袭性,称之为“近端型”上皮样肉瘤。本文报告1例16岁女性患者,其症状初期表现为左侧颊部进行性肿胀伴疼痛,在进行专科检查及影像学检查后,初步考虑为左侧上颌窦内恶性肿瘤,伴局部骨质破坏。随后根据其组织病理学表现和免疫组织化学特征,最终确诊为近端型上皮样肉瘤。对该患者进行左上颌骨次全切除术,术后随访1 a,未见复发和转移迹象。
Epithelioid sarcoma is a very rare histological type of soft tissue sarcoma, often manifesting in the subcutaneous tissue or intradermal masses of the adolescent limb. One type has a high degree of invasiveness and is called a “near type” epithelioid sarcoma. This article reports a 16-year-old female patient whose symptoms were initially characterized by progressive swelling of the left cheek with pain. After specialist examinations and imaging studies, he initially considered malignant tumors in the left maxillary sinus with localized bone destruction. . Subsequently, according to histopathological findings and immunohistochemical features, the final diagnosis was a proximal type of epithelioid sarcoma. The patient underwent a subtotal resection of the left maxilla and followed up for 1 year. There was no sign of recurrence or metastasis.