嗜血细胞综合征(HPS)是一类多器官、多系统受累,并进行性加重伴免疫功能紊乱的巨噬细胞增生性疾病,病死率极高[1-2]。近年来,HPS在临床不再是罕见病,这一方面与临床诊治水平的提高有关,另一方面可能该病在我国的发病率确实有所增高。近期,我们回顾分析了HPS伴肝功能异常28例的临床资料,分析其临床特征及误诊原因。现分析报告如下。 Hemophilus syndrome (HPS) is a multi-organ, multi-system involvement and progressive aggravation of immune dysfunction macrophage proliferative disease, high mortality [1-2]. In recent years, HPS is no longer a rare clinical disease, on the one hand, with the improvement of clinical diagnosis and treatment, on the other hand may be the incidence of the disease in our country has indeed increased. Recently, we retrospectively analyzed the clinical data of 28 HPS patients with liver dysfunction and analyzed their clinical characteristics and causes of misdiagnosis. The analysis report is as follows.