目的探讨畸胎型髋关节脱位的治疗方法。方法在1995年8月~2003年11月期间,我科收治畸胎型髋关节脱位8例,全部病例均为男性,左髋3例,右髋2例,双髋3例。年龄1.5~6岁,平均4岁。采用髋关节Bikini入路,髋关节切开复位的同时进行骨盆截骨及股骨近端短缩旋转内翻截骨术治疗畸胎型髋关节脱位8例11个髋关节。结果本组病例随诊时间1~8年。8例中3例步态基本正常,4例轻度跛行,1例明显跛行。3个髋关节活动基本正常,6个髋关节活动轻度受限,2个髋关节部分僵硬。临床评定3个髋关节为优,6个髋关节为良,2个髋关节为中。X线片结果3个髋关节为优,5个髋关节为良,3个髋关节为中。没有再脱位,但有3个髋关节发生股骨头缺血性坏死。结论通过髋关节Bikini入路,切开复位的同时进行相应的骨盆截骨及股骨近端短缩旋转内翻截骨术是治疗畸胎型髋关节脱位的有效方法之一。 Objective To investigate the treatment of teratoid hip dislocation. Methods Between August 1995 and November 2003, 8 cases of teratoid hip dislocation were treated in our department. All cases were male, 3 cases were left hip, 2 cases were right hip and 3 cases were double hip. Age 1.5 to 6 years old, average 4 years old. Hip joint Bikini approach was used to treat terato-femoral dislocation in 8 cases and 11 hips in the same time with hip osteotomy and pelvic osteotomy and proximal femoral shortening. Results The patients were followed up for 1 to 8 years. Three of the eight patients had a normal gait, four with mild claudication and one with obvious claudication. The activities of the three hip joints were basically normal, the activities of the six hip joints were slightly limited, and the two hip joints were partially stiff. Clinical assessment of 3 hip is excellent, 6 hip is good, 2 hip is medium. X-ray results 3 hip is excellent, 5 hip is good, 3 hip is medium. No further dislocation, but there are 3 hip joint avascular necrosis. Conclusions Through the Bikini approach to the hip joint, the corresponding pelvic osteotomy and proximal femur rotatory varus osteotomy are one of the effective methods for the treatment of teratoid hip dislocation.