先天性凝血因子Ⅶ缺乏症极少见,国内仅有少数报告,我院去年发现一例,介绍如下。 李××,男,8岁,湖南耒阳人,汉族。住院号289906。二岁起反复皮下紫癜、鼻衄、牙龈出血。近二年来先后10次左膝、踝关节肿痛,活动受限,曾先后几次因出血在当地医院一般药物治疗无效。输父血可以止血。近日出现双下肢紫癜、血尿。 Congenital coagulation factor Ⅶ deficiency rare, only a handful of domestic reports, our hospital found a case last year, described below. Li × ×, male, 8 years old, Hunan Xingyang, Han nationality. Hospitalization number 289906. Repeated subcutaneous purpura from age two, epistaxis, bleeding gums. Over the past two years has 10 times the left knee, ankle swelling and pain, limited mobility, has several times due to bleeding in the local hospital general drug treatment is invalid. Father fathers can stop bleeding. Recently appeared double lower extremity purpura, hematuria.