论文部分内容阅读
目的采用超声心动图对先天性矫正型大动脉转位(ccTGA)的解剖特征进行分析。方法超声心动图检查,且诊断为ccTGA的患儿45例,采用Van Praagh顺序节段分析法进行诊断。结果 (1)心房-心室连接不一致、心室-大动脉连接不一致:{S,L,L}40例(包括左位心30例,孤立性右位心10例);{I,D,D}4例(包括左位心2例,镜像右位心2例);{S,L,D}1例,为左位心。(2)合并房室瓣异常:房室瓣结构畸形7例。(3)其他合并畸形40例(88.9%),其中,最常见的是肺动脉瓣狭窄或肺动脉瓣下狭窄(29例,64.4%)和室间隔缺损(25例,55.6%)。结论 {S,L,L}是ccTGA最常见的病理解剖形式,此外也可以表现为{I,D,D}和{S,L,D};在ccTGA患者中,解剖三尖瓣功能性反流较常见且较严重;肺动脉瓣狭窄或肺动脉瓣下狭窄和室间隔缺损是其最常见的合并畸形。
Objective To analyze the anatomic features of congenital orthopedic aortic transposition (ccTGA) using echocardiography. Methods Echocardiography was performed in 45 children diagnosed with ccTGA and was diagnosed by Van Praagh sequential segment analysis. Results (1) Atrial-ventricular connections were inconsistent and ventricular-aorta connections were inconsistent: {S, L, L} 40 (including 30 cases of left locus and 10 cases of isolated right locus); Cases (including left centroid in 2 cases, mirror right centroid in 2 cases); {S, L, D} in 1 case, left centrum. (2) with atrioventricular valve anomalies: atrioventricular valve malformations in 7 cases. (3) Other 40 cases (88.9%) had combined malformations, of which the most common were pulmonary valve stenosis or pulmonary valve stenosis (29 cases, 64.4%) and ventricular septal defect (25 cases, 55.6%). Conclusion {S, L, L} is the most common histopathological form of ccTGA. In addition, it can be expressed as {I, D, D} and {S, L, D} Flow is more common and more serious; pulmonary valve stenosis or pulmonary valve stenosis and ventricular septal defect is its most common combined deformity.