目的　探讨血管母细胞瘤的诊断和治疗。方法　回顾性分析经神经外科手术和病理证实的 44例资料。结果　 41例获术前确诊。肿瘤全切 3 7例 ,手术死亡 4例。结论　实质性血管母细胞瘤仍是神经外科较难处理的肿瘤 ,忌作活检和分块切除 ,应在离断供血动脉后切除肿瘤。CT和MRI是术前诊断血管母细胞瘤的主要方法 ,术中应用特殊的显微外科技术可提高手术疗效 Objective To investigate the diagnosis and treatment of hemangioblastoma. Methods Retrospective analysis of 44 cases confirmed by neurosurgery and pathology. Results 41 cases were diagnosed preoperatively. Totally 37 cases of tumor, surgical death in 4 cases. Conclusions Substantial hemangioblastoma is still a neurosurgical tumor that is difficult to treat. It should not be biopsied or subcutaneously resected. The tumor should be excised after the artery is severed. CT and MRI is the main method of preoperative diagnosis of hemangioblastoma, the application of special microsurgical techniques can improve the surgical efficacy