巴特氏综合征(简称巴氏征)是临床上较为少见的一种有关肾脏内分泌的疾病,过去由于缺乏对它的认识与注意,因此往往可能被漏诊或误诊,自1962年巴特氏首先报告两例患者以来,近几年来有关巴氏征的报告不断增多,且临床表现日趋复杂,目前在国外已开展了对本病的多方面研究,直到现在还未能肯定其确切病因及发病机理,尽管如此,文献上现已将巴氏征列为单独一类 Bart’s syndrome (referred to as Pakistan’s sign) is a clinically rare kidney endocrine disease, the past due to lack of awareness and attention to it, it may often be missed or misdiagnosed, since 1929, Barthes first reported two Cases of patients, in recent years, reports of Pakistani signs of increasing, and increasingly complex clinical manifestations, has been carried out in many foreign studies of the disease, until now the exact etiology and pathogenesis has not been confirmed, though Thus, the literature has now been classified as a separate category of Pakistan