先天性青光眼并发视网膜脱离首由Axenfeld描述,认为在这种情况下,视网膜脱离常是致盲的决定性因素。作者报告18例先天性青光眼合并视网膜脱离的临床特征及手术效果。病例分为单纯的和并发的。单纯先天性青光眼指无其他发育异常且有典型的房角镜改变者;并发者则指有其他发育缺陷的病例。18例不同原因的先天性青光眼,发生视网膜脱离者21眼,男13例,女5例;单纯性16例,并发性2例。 Congenital glaucoma with retinal detachment was first described by Axenfeld, in which case retinal detachment is often the determining factor for blinding. The authors report 18 cases of congenital glaucoma with retinal detachment clinical features and surgical results. Cases are divided into simple and concurrency. Pure congenital glaucoma means no other dysplasia and typical changes in the gonioscopy; concurrency refers to other cases of developmental defects. 18 cases of congenital glaucoma of different causes, retinal detachment in 21 eyes, 13 males and 5 females; simple in 16 cases, complicated in 2 cases.