临床上遇到出血性疾病,在确诊方面可有一定困难;一则由于各病易于混淆,另外,也涉及到实验室检查条件。第Ⅴ因子缺乏症是非常罕见的,本文报告一例。笔者借此病例复习文献,提出分辨不同的凝血因子缺乏症的梗概;最后重点讨论本病与特别有关的凝血因子缺乏症的鉴别诊断,并对本病予以较详细的介绍。 Hemorrhagic disease is clinically encountered and may be difficult to diagnose; one is confusing because of the various illnesses and, in addition, involves laboratory tests. Factor V deficiency is very rare, this article reports a case. The author of this case review of the literature, put forward to distinguish different coagulation factor deficiency outline; Finally, the focus of this disease and particularly related to the differential diagnosis of coagulation factor deficiency, and the disease to be more detailed introduction.