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目的:了解掌跖角化一牙周破坏综合征(PLS)临床诊断与治疗。方法:收集并调查一例掌跖角化一牙周破坏综合征病例,进行家谱分析,对其进行全口义齿修复。并对相关文献进行回顾。结果:掌跖角化一牙周破坏综合征是一种罕见的以严重牙周组织破坏及掌跖、膝盖、肘部等部位皮肤过度角化为特征的常染色体隐性遗传病,发病年龄早,最终可导致全口牙列缺失。全口义齿修复可获得较满意的效果。结论:早期发现、早期治疗对改善PLS的预后是非常重要的。
Objective: To understand the clinical diagnosis and treatment of palmoplantar keratosis and periodontal syndrome (PLS). Methods: A case of periodontal disruption syndrome of palmoplantar keratoderma was collected and investigated. Pedigree analysis was performed and the complete denture was repaired. And review the relevant literature. Results: The paw parakeratosis and periodontal syndrome is a rare autosomal recessive disease characterized by severe periodontal tissue destruction and hyperkeratosis of the skin such as palmoplantar, knee and elbow. The age at onset , Can eventually lead to missing the entire dentition. Complete denture repair can be more satisfactory results. Conclusion: Early detection and early treatment are very important to improve the prognosis of PLS.