目的:囊性纤维化(cystic fibrosis,CF)患者病程中常伴发渐进性肺动脉高压.本研究旨在探讨MRI流体测量技术(MR速度编码技术)对检出囊性纤维化患者肺动脉高压的价值。方法:48例(年龄10~40岁,平均16岁;男23例,女25例)不同程度(第一秒最大呼气量FEV1与预计值比值为74%±23%)囊性纤 Objective: Cystic fibrosis (CF) patients often accompanied by progressive pulmonary hypertension in the course of the disease.The purpose of this study was to investigate the value of MRI fluid measurement technique (MR speed coding technique) for the detection of pulmonary hypertension in patients with cystic fibrosis. Methods: Forty-eight patients (aged 10-40 years old, average 16 years old, 23 males and 25 females) of varying degrees (first-second maximal expiratory volume FEV1 was 74% ± 23% of expected value)