肝门脉硬化(hepatic portal sclerosis,HPS)是由于门静脉主干或分支非特异性炎症引起血管内径变窄、血流阻塞,临床表现为门脉高压伴脾肿大、贫血而无肝硬化、肝外门静脉阻塞的一组综合征,也有人称之为非硬化性门静脉纤维化、非硬化性门脉高压或特发性门脉高压等[1]。其诊断依据 Hepatic portal sclerosis (HPS) is caused by non-specific portal vein or non-specific inflammation caused by vascular diameter narrowing, obstruction of blood flow, clinical manifestations of portal hypertension with splenomegaly, anemia without cirrhosis, extrahepatic portal vein A group of obstructive syndrome, also known as non-sclerosing portal vein fibrosis, non-sclerosing portal hypertension or idiopathic portal hypertension [1]. The diagnosis based on