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本文分析组织细胞增生症Ｘ２１例的诊治情况：局限型（骨骼嗜酸性肉芽肿）１１例仅眶骨单灶受累，手术治疗预后良好；慢性播散型（Ｈ－Ｓ－Ｃ病）８例除眶骨受累外，尚有骨髓损害、皮肤损害、肝脾淋巴结肿大和尿崩症等全身改变，追踪６例有３例死亡；急性播散型（Ｌ－Ｓ病）２例无眶骨受累，均为全身损害，于病发２年内死亡。作者对组织细胞增生症Ｘ的临床分型、发病年龄、骨受累、眼球突出、全身病变及治疗和预后，作了重点讨论。
This article analyzes the diagnosis and treatment of X21 cases of histiocytosis: limited type (bone eosinophilic granuloma) in 11 cases only orbital bone involvement, surgical treatment of good prognosis; chronic disseminated (H-S-C disease) in 8 cases Orbital bone involvement, there are bone marrow damage, skin lesions, liver and spleen lymph nodes and diabetes insipidus and other systemic changes, 6 cases were followed up for 3 deaths; acute disseminated (L-S disease) 2 cases without orbital bone involvement, All are systemic damage, died within 2 years of onset. The author of histiocytosis X clinical classification, age of onset, bone involvement, prominence, systemic disease and treatment and prognosis, made a focused discussion.