先天性纯红细胞性贫血是一种罕见的贫血,大多于婴幼儿期出现.自从1936年由Josephs发现这类型贫血以来,见于国际医学资料报告者,至今仅有100多例,而国内报告更少.现将我科所见一例,结合文献复习报告如下: Congenital pure red blood cell anemia is a rare anemia that occurs mostly in infancy and has been reported by international medical information authors since Josephs discovered this type of anemia in 1936. So far only 100 cases have been reported and fewer have been reported in the country Now we see an example of the case, combined with the literature review report is as follows: