目的通过报道少见的神经系统疾病-脑三叉神经血管瘤病(Sturge-weber综合征,也称脑-面部血管瘤病),引起同行对该病的认识和重视。方法对脑三叉神经血管瘤病进行回顾性分析并文献复习。结果经过临床物理检查及仪器辅助检查,该病例被确诊为脑三叉神经血管瘤病。结论治疗主要是对惊厥发作、青光眼等对症治疗,若惊厥难以控制时,可考虑外科切除病变的脑组织。 OBJECTIVES Awareness and importance of this disease are aroused by colleagues by reporting a rare neurological disease called Sturge-weber syndrome (also called brain-facial hemangiomatosis). Methods Retrospective analysis and literature review of brain trigeminal neovascular disease. The results of clinical physical examination and laboratory tests, the case was diagnosed as cerebral trigeminal neovascular disease. Conclusion The treatment is mainly for seizures, glaucoma and other symptomatic treatment, if convulsions are difficult to control, consider the surgical removal of brain tissue lesions.