目的　探讨先天性白内障术后视网膜脱离的特点及手术方法。　方法　对 42例先天性白内障患者 44只白内障术后孔源性视网膜脱离眼的临床资料进行回顾分析 ,比较不同的视网膜脱离手术方法治疗后的效果。先天性白内障术后发生视网膜脱离平均间隔时间为 14.8年。绝大多数白内障手术为吸出术并有后囊膜切开史 ;多数瞳孔不能散大并有后发性白内障形成。 16只眼曾测眼轴 ,平均轴长 (2 6 .80±1.90 ) mm。视网膜脱离手术前裂孔发现率仅 43.2 %。　结果　巩膜手术成功率 80 .3% ,玻璃体手术成功率85 .7%。　结论　先天性白内障术后发生视网膜脱离间隔时间长 ;因瞳孔因素 ,周边眼底检查困难 ,巩膜手术成功率低 ,玻璃体手术是较理想的手术方式。 Objective To investigate the characteristics and surgical methods of retinal detachment after congenital cataract surgery. Methods The clinical data of 44 eyes with rhegmatogenous retinal detachment after cataract surgery in 42 patients with congenital cataract were retrospectively analyzed. The effects of different methods of retinal detachment surgery were compared. Congenital cataracts retinal detachment occurred after the average interval of 14.8 years. The vast majority of cataract surgery for aspiration and posterior capsule incision history; most pupils can not be dispersed and have a posterior cataract formation. 16 eyes had axial length measured, the average axial length (26.880 ± 1.90) mm. Retinal detachment preoperative hole detection rate was only 43.2%. Results The success rate of scleral surgery was 80.3%, the success rate of vitreous surgery was 85.7%. Conclusions The retinal detachment is a long time interval after congenital cataract surgery. Due to the pupillary factors, peripheral retinal examination is difficult and the success rate of scleral surgery is low. Vitreous surgery is an ideal surgical method.