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患获得性血管性假血友病(AVWD)的病人常有严重的出血,治疗非常困难。作者报道1例AVWD患者接受大的矫形手术,未用替代疗法,而用大剂量静脉用丙种球蛋白(IVIg)取得成功。病例报告患者56岁,男性。1985年2月患脊椎浆细胞瘤,IgGK轻链型,APTT正常。1987年3月,发生反复自发性消化道出血所致贫血症。既往曾接受过几次手术而无出血史,家
Patients with acquired von Willebrand disease (AVWD) often have severe bleeding and treatment is very difficult. The authors report that one of the patients with AVWD underwent major orthopedic surgery without replacement therapy and successfully treated with intravenous gammaglobulin (IVIg) at a high dose. Case Report Patient 56 years old, male. February 1985 suffering from spinal plasma cell tumor, IgGK light chain, APTT normal. March 1987, repeated spontaneous gastrointestinal bleeding caused by anemia. Have received a few previous surgery without bleeding history, home