急性脑病合并内脏脂肪变性综合征又称Reye综合征(Reye Syndrome,RS)是一种以急性脑病和肝脏脂肪变性为主要临床特征的综合征,1963年由Reye等首先报道[1]。Reye综合征是儿科的一种危重疾患,常在前驱病毒感染后出现急性颅内压增高、意识障碍和惊厥等脑病症状。常伴有严重脑水肿, Acute encephalopathy with visceral steatosis syndrome Reye syndrome (Reye Syndrome, RS) is a syndrome characterized by acute encephalopathy and hepatic steatosis as the main clinical features, first reported by Reye et al in 1963 [1]. Reye syndrome is a critical disorder in pediatrics, often with symptoms of encephalopathy such as increased intracranial pressure, impaired consciousness and convulsions after a precursor virus infection. Often accompanied by severe brain edema,