目的　探讨烟雾病合并颅内动脉瘤的临床特点 ,以提供临床治疗依据。方法　回顾性分析 10例烟雾病合并颅内动脉瘤患者的临床表现、动脉瘤位置及治疗方法。结果　 10例中 8例表现为颅内出血 ,2例表现为缺血症状 ;8个动脉瘤位于Willis环周围 ,1个位于基底节 ,1个位于椎动脉 ;其中 6例 (7个动脉瘤 )行外科治疗 ,均获良好疗效。结论　烟雾病合并动脉瘤根据其位置的不同 ,可分为累及Willis环的动脉瘤和累及侧支或烟雾病血管的动脉瘤。建议对Willis环周围的动脉瘤进行外科手术治疗 ,对基底节或侧支血管的动脉瘤可予对症保守治疗 Objective To explore the clinical features of moyamoya disease complicated with intracranial aneurysms to provide the basis for clinical treatment. Methods Retrospective analysis of 10 cases of moyamoya disease with intracranial aneurysm clinical manifestations, aneurysm location and treatment. Results Eight of the 10 patients showed intracranial hemorrhage and two showed ischemic symptoms. Eight aneurysms were located around the Willis ring, one in the basal ganglia and one in the vertebral artery. Six of them (seven aneurysms) Surgical treatment, were good effect. Conclusions Moyamoya disease with aneurysm can be divided into aneurysms involving Willis ring and aneurysms involving blood vessels of collaterals or moyamoya depending on its location. It is recommended that surgical treatment of aneurysms around the Willis ring, symptomatic conservative treatment of the aneurysm of the basal ganglia or collateral vessels