原发性眼内淋巴瘤是一种眼部相对少见的高度恶性的非霍奇金淋巴瘤,属于原发性中枢神经系统淋巴瘤,近年来发病呈上升趋势,其临床诊断有一定难度。本文对原发性眼内淋巴瘤的流行病学、临床表现、影像学检查、细胞学和组织病理学检查,生化和分子生物学检查、鉴别诊断、治疗和预后等进行综述。 Primary intraocular lymphoma is a relatively rare eye, a highly malignant non-Hodgkin’s lymphoma, is a primary central nervous system lymphoma, the incidence is on the rise in recent years, the clinical diagnosis of a certain degree of difficulty. This article reviews the epidemiology, clinical manifestations, imaging examination, cytology and histopathology, biochemical and molecular biological examination, differential diagnosis, treatment and prognosis of primary intraocular lymphoma.