新生儿乳糜胸是新生儿期比较罕见的疾病,但却是新生儿胸腔积液最常见的原因,发病率估计为1/10000[1-2],Pisek在1917年首先描述此病。本病是由于胸导管或胸腔内大淋巴管破裂或阻塞导致淋巴液即乳糜在胸腔的异常积聚,并引起严重的呼吸、营养以及免疫障碍的一种疾病。近年来,随着 Neonatal chylothorax is a relatively rare disease in the neonatal period, but it is the most common cause of neonatal pleural effusion. The incidence is estimated at 1 in 10,000 [1-2] and Pisek first described the disease in 1917. The disease is due to thoracic or intrathoracic lymphatic rupture or obstruction caused by the lymphatic fluid that chylothorax abnormal accumulation, and cause serious respiratory, nutritional and immune disorders of a disease. In recent years, with