目的　分析和探讨婴幼儿椎管内肿瘤的临床特点、早期诊断和手术治疗。方法　对 6 3例婴幼儿椎管内肿瘤的临床资料进行回顾性研究。结果　本组病例皮样囊肿和表皮样囊肿占41.3% ,脂肪瘤 12 .7% ,畸胎瘤 7.9% ,肠源性囊肿 5 .0 % ,神经母细胞瘤占 4.8% ,其他恶性肿瘤占4.8%。手术全切除率为 76 .7% ,大部分切除率为 18.3% ,部分切除率为 5 .0 %。肢体运动障碍者 ,术后随诊时 78.9%好转 ,感觉障碍 6 4%改善 ,括约肌功能障碍 6 3.3%改善 ,全组无死亡。结论　婴幼儿椎管内肿瘤以先天性肿瘤为主 ,对其应早期诊断和早期手术治疗 ,大多能做到肿瘤全切除 ,术后症状缓解 ,能明显提高患儿生活质量 Objective To analyze and discuss the clinical features, early diagnosis and surgical treatment of infantile spinal canal tumor. Methods The clinical data of 63 cases of infantile spinal canal tumors were retrospectively studied. Results The dermoid and epidermoid cysts in this group accounted for 41.3%, lipoma 12.7%, teratoma 7.9%, enterogenous cyst 5.0%, neuroblastoma 4.8%, other malignant tumors 4.8 %. Surgical resection rate was 76.7%, the majority of resection rate was 18.3%, partial resection rate was 5.0%. Acromegaly, 78.9% improvement after surgery, sensory disturbance 64% improvement, sphincter dysfunction 6 3.3% improvement, the whole group without death. Conclusions Infantile spinal canal tumors are mainly congenital tumors, which should be diagnosed early and early surgical treatment, most of which can achieve tumor resection, postoperative symptom relief, can significantly improve children’s quality of life