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甲型血友病(HA)是一种由于遗传性凝血因子Ⅷ缺乏或其功能缺乏所引起的出血性疾病。目前尚无根治性治疗手段,因受经济条件以及凝血因子缺乏等因素的制约,按需替代治疗仍然是我国目前HA最有效的治疗手段,但存在使用不便、疾病传播和抑制物产生等不足情况。因此,深入探索血友病家庭治疗的综合关怀模式至关重要,治愈血友病患者的理想方法是基因治疗,但仍存在安全性等问题,它还需要进一步的研究,以达到完全治愈血友病的目的。
Hemophilia A (HA) is a hemorrhagic disease caused by lack of hereditary factor Ⅷ or its lack of function. At present there is no radical treatment because of economic conditions and the lack of factors such as clotting factors, on-demand replacement therapy is still the most effective treatment of HA in our country, but there are inconveniences, disease transmission and inhibitors and other shortcomings . Therefore, it is very important to thoroughly explore the comprehensive care mode for hemophilia family therapy. The ideal way to cure hemophiliacs is gene therapy. However, there are still some problems such as safety. It needs further research to completely cure hemophilia The purpose of the disease.