目的探讨韧带样型纤维瘤(desmoid-type fibromatoses,DF)的影像学特征。方法回顾性分析经手术及病理证实的20例DF患者的影像和临床资料,其中原发性DF 13例,复发性7例。探讨其CT和MRI影像学特征。结果 20例DF均单发,其中12例(60.0%)边界不清,9例(45.0%)包绕血管神经,8例(40.0%)有骨膜粘连。10例行CT检查,平扫呈稍低密度,密度均匀,瘤内未见钙化及坏死区。增强扫描6例表现为中度强化,延迟扫描5例呈渐进性强化。15例行MRI检查,T1WI呈等或稍低信号,T2WI呈高于肌肉低于脂肪信号,增强扫描11例呈中等或明显不均匀强化,并随着各期相渐进性强化。其中9例(81.8%)可见条索状或小斑片状T1WI及T2WI低信号,增强后未见强化。扩散加权成像(DWI)扫描2例呈高信号,表观扩散系数(ADC)图上呈等或稍高于肌肉信号。结论 DF的CT、MRI表现具有一定特征,MR增强、动态增强及DWI扫描对DF的诊断及预后监测具有重要价值。 Objective To investigate the imaging features of desmoid-type fibromatoses (DF). Methods The images and clinical data of 20 patients with DF confirmed by surgery and pathology were retrospectively analyzed. Among them, 13 were primary DF and 7 were recurrent. To investigate the CT and MRI imaging features. Results All the 20 cases of DF were solitary. Among them, 12 cases (60.0%) had unclear boundary, 9 cases (45.0%) surrounded the vascular nerves and 8 cases (40.0%) had periosteal adhesions. 10 cases underwent CT examination, showed a slightly lower density, uniform density, no calcification and necrosis in the tumor area. Enhanced scanning in 6 cases showed moderate enhancement, delayed scanning in 5 cases were progressive enhancement. Fifteen patients underwent MRI examination with equal or slightly lower signal on T1WI, T2WI higher than muscle under fat signal, enhanced enhancement in 11 cases with moderate or obvious non-uniform enhancement and progressive enhancement with each phase. Among them, 9 cases (81.8%) showed low signal of cord-like or patchy T1WI and T2WI without enhancement. Diffusion - weighted imaging (DWI) scans showed high signal in 2 cases and apparent or slightly higher than muscle signal in apparent diffusion coefficient (ADC). Conclusion The CT and MRI features of DF have certain characteristics. MR enhancement, dynamic enhancement and DWI scan are of great value in the diagnosis and prognosis monitoring of DF.