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目的探讨儿童嗜铬细胞瘤的临床特点及诊治方法。方法对1984～2004年诊治的8例儿童嗜铬细胞瘤进行回顾性分析。术前通过临床表现、24h尿儿茶酚胺、131碘间碘苄胍全身核素扫描(131IMIBG扫描)、B超或CT检查明确定性及定位诊断。并用α受体阻滞剂行术前药物准备。结果8例均行手术切除肿瘤;病理诊断:良性5例,恶性3例。结论儿童嗜铬细胞瘤少见,病情进展快;早期诊断、手术切除是目前惟一可治愈的方法。
Objective To investigate the clinical features and diagnosis and treatment of pheochromocytoma in children. Methods Eight children with pheochromocytoma diagnosed and treated from 1984 to 2004 were retrospectively analyzed. Preoperative clinical manifestations, 24h urinary catecholamines, iodine 131 Iodine guanidine whole body radionuclide scanning (131IMIBG scan), B ultrasound or CT examination of a clear qualitative and positional diagnosis. Preoperative drug preparation with α-blocker. Results Eight cases underwent surgical resection of the tumor. The pathological diagnosis was benign in 5 cases and malignant in 3 cases. Conclusions Children with pheochromocytoma are rare and their condition progresses rapidly. Early diagnosis and surgical resection are the only methods that can be cured.