睾丸内肾上腺残余瘤(TART)是睾丸内异位的肾上腺残基过度增殖性良性病变,是先天性肾上腺皮质增生症(CAH)并不少见的并发症,是导致CAH男性患儿成年后睾丸功能障碍及生育力降低的主要原因之一。早期诊断和治疗可避免不可逆的睾丸功能损害。对TART的发病机制、临床表现和分期、诊断及治疗进展集中阐述很有必要。 Testicular adrenal remnant tumor (TART) is a benign adrenal hyperplastic benign lesions of the testis, is not uncommon complications of congenital adrenal hyperplasia (CAH), is caused by testicular function in adult children with CAH Obstacles and fertility reduced one of the main reasons. Early diagnosis and treatment can avoid irreversible damage to the testes. The pathogenesis of TART, clinical manifestations and staging, diagnosis and treatment of intensive progress is necessary.